CLINICAL CASE OF SUCCESSFUL TREATMENT OF A PATIENT WITH AORTIC ROOT ANEURYSM AND PULMONARY ARTERY STENOSIS AFTER RADICAL CORRECTION OF PULMONARY ARTERY ATRESIA WITH VENTRICULAR SEPTAL DEFECT

Highlights

The article presents a clinical case of successful treatment of a patient with aortic root aneurysm and pulmonary artery stenosis after radical three-stage repair of pulmonary atresia with ventricular septal defect.

Abstract

Aortic root aneurysm with aortic regurgitation is a rare cause of re-operation in patients who have had primary repair of pulmonary atresia with ventricular septal defect or tetralogy of Fallot. Recently, due to an increase in cases of primary radical treatment of congenital cardiac surgery and life expectancy of these patients, the number of cases of re-operation due to aortic root dilatation has also increased. One of the main reasons for long-term aortic regurgitation and of aortic root enlargement is the presence of a subaortic ventricular septal defect below the aortic valve, which deforms the aortic annulus geometry and changes intra-aortic hemodynamics. All of these factors make the aortic root surgical reconstruction just a question of time. This is a real challenge for both adult and pediatric heart surgeons, requiring a team approach. This article presents a clinical case of successful treatment of a patient with aortic root aneurysm, aortic regurgitation with concomitant pulmonary conduit restenosis and residual ventricular septal defect who underwent a three-stage repair of pulmonary atresia and ventricular septal defect.

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