A RARE CASE OF ALCAPA SYNDROME IN AN ADOLESCENT
https://doi.org/10.17802/2306-1278-2019-8-3-142-148
Abstract
The article is aimed to analyze the causes of delayed diagnosis of congenital heart disease. A rare case of abnormal originating of the left coronary artery from pulmonary artery in an adolescent is reported. Both, clinical manifestations of circulatory insufficiency and diagnostic challenges, are described. All routine medical records and data were reviewed. Cardiac anatomy and age-related clinical symptoms are described with the subsequent discussion of the surgical treatment. The approach to differential diagnosis is presented. The factors contributing to the delayed diagnosis of the CHD are analyzed.
About the Authors
S. A. Shmulevich
State Budgetary Healthcare Institution of the Kemerovo Region “Kemerovo Regional Clinical Cardiology Dispensary n.a. Academician L.S. Barbarash”
Russian Federation
Russian Federation
Shmulevich Svetlana A., PhD, Head of the Pediatric Cardiology Department
6, Sosnoviy Blvd., Kemerovo, 650002
I. N. Sizova
Federal State Budgetary Institution “Research Institute for Complex Issues of Cardiovascular Diseases”
Russian Federation
Russian Federation
Sizova Irina N., PhD, senior researcher at the Laboratory of Ultrasound and Electrophysiological Methods of Diagnosis
6, Sosnoviy Blvd., Kemerovo, 650002
S. A. Makarov
State Budgetary Healthcare Institution of the Kemerovo Region “Kemerovo Regional Clinical Cardiology Dispensary n.a. Academician L.S. Barbarash”
Russian Federation
Russian Federation
Makarov Sergey A., PhD, Medical Director
6, Sosnoviy Blvd., Kemerovo, 650002
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Review
For citations:
Shmulevich S.A., Sizova I.N., Makarov S.A. A RARE CASE OF ALCAPA SYNDROME IN AN ADOLESCENT. Complex Issues of Cardiovascular Diseases. 2019;8(3):142-148. (In Russ.) https://doi.org/10.17802/2306-1278-2019-8-3-142-148
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