A clinical case of an anomalous origin of the left coronary artery from the pulmonary artery (Bland-White-Garland syndrome) in an adult patient
https://doi.org/10.17802/2306-1278-2022-11-3-199-203
Abstract
Highlights. The paper presents a unique clinical case of patient with congenital heart defect known as Bland-White-Garland syndrome diagnosed in the adulthood. Takeuchi repair (creation an intrapulmonary tunnel) was carried out to treat this defect.
Background. An anomalous origin of the left coronary artery from the pulmonary artery (Bland-White-Garland syndrome) is an uncommon but severe pathology that requires immediate surgical treatment. The use of modern diagnostic methods (both non-invasive and invasive) has resulted in higher prevalence of this syndrome, diagnosed not only in an early childhood, but also in adulthood. Recording each medical case and choosing an optimal treatment strategy will increase knowledge of this pathology and reduce the high risk of mortality. The paper presents a clinical case of this syndrome in an adult patient who had remained undiagnosed for a long time as the syndrome was masked under the clinical features of chronic heart failure. Takeuchi repair (creation an intrapulmonary tunnel) was carried out to treat this extremely rare defect for a patient of this age group.
About the Authors
A. O. Povoroznyi
Republican Clinical Hospital named after N.A. Semashko
Russian Federation
Competing Interests:
Russian Federation
Andrey O. Povoroznyi - Cardiovascular Surgeon at the Republican Clinical Hospital named after N.A. Semashko.
69, Kievskaya St., Simferopol, Republic of Crimea, 295017.
Competing Interests:
Автор заявляет об отсутствии конфликта интересов.
E. A. Zakharyan
V.I. Vernadsky Crimean Federal University
Russian Federation
Competing Interests:
Russian Federation
Elena A. Zakharyan - PhD, Associate Professor at the Department of Internal Medicine № 1, Medical Academy named after S.I. Georgievsky, V.I. Vernadsky Crimean Federal University.
4, Vernadskogo Ave., Simferopol, Republic of Crimea, 295007.
Competing Interests:
Автор заявляет об отсутствии конфликта интересов.
P. E. Maksimova
V.I. Vernadsky Crimean Federal University
Russian Federation
Competing Interests:
Russian Federation
Polina E. Maksimova - fifth-year student at the Medical Academy named after S.I. Georgievsky, V.I. Vernadsky Crimean Federal University.
4, Vernadskogo Ave., Simferopol, Republic of Crimea, 295007.
Competing Interests:
Автор заявляет об отсутствии конфликта интересов.
J. T. Keremov
Almazov National Medical Research Centre of the Ministry of Health of the Russian Federation
Russian Federation
Competing Interests:
Russian Federation
Jalil T. Keremov - Cardiovascular Surgeon at the Almazov National Medical Research Centre of the Ministry of Health of the Russian Federation.
2, Akkuratova St., St. Petersburg, 197341.
Competing Interests:
Автор заявляет об отсутствии конфликта интересов.
O. A. Kazanceva
Republican Clinical Hospital named after N.A. Semashko
Russian Federation
Competing Interests:
Russian Federation
Oksana A. Kazanceva - Cardiologist at the Republican Clinical Hospital named after N.A. Semashko.
69, Kievskaya St., Simferopol, Republic of Crimea, 295017.
Competing Interests:
Автор заявляет об отсутствии конфликта интересов.
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Review
For citations:
Povoroznyi A.O., Zakharyan E.A., Maksimova P.E., Keremov J.T., Kazanceva O.A. A clinical case of an anomalous origin of the left coronary artery from the pulmonary artery (Bland-White-Garland syndrome) in an adult patient. Complex Issues of Cardiovascular Diseases. 2022;11(3):199-203. (In Russ.) https://doi.org/10.17802/2306-1278-2022-11-3-199-203
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