THE 1st STAGE OF HEMODYNAMIC STRATEGIES FOR MANAGEMENT OF HYPOPLASTIC LEFT HEART SYNDROME
Ekaterina N. Amansakhatova,
Ilya A. Soynov,
Yuriy Yu. Kulyabin,
Nataly R. Nichay,
Kseniya A. Rzaeva,
Olga S. Anikina,
Ilya A. Velyukhanov,
Alex N. Arkhipov https://doi.org/10.17802/2306-1278-2026-15-1-109-125
Abstract
Highlights
The research presented in this paper evaluates the alternatives for the 1st stage of hemodynamic correction of HLHS, outlines possible complications that may emerge in the postoperative phase, and provides approaches for their overcome in the intraoperative period.
Abstract
Hypoplastic left heart syndrome (HLHS) is a congenital heart disease that describes in the underdevelopment of the left-sided structures of the heart. HLHS is a rare defect in infants born and occurs in 2–3% of all congenital heart diseases. Primary heart transplantation demonstrates a radical correction of HLHS. However, a shortage of organs and a prohibition on this procedure to juvenile make it unavailable. Therefore, this review presents options for surgical correction of newborns with hypoplastic left heart syndrome, their advantages and disadvantages, as well as possible complications.
About the Authors
Ekaterina N. Amansakhatova
Meshalkin National Medical Research Center;
Novosibirsk State University
Russian Federation
Russian Federation
Research Intern, Department of Congenital Heart Disease Research, Resident Physician in Cardiovascular Surgery, Meshalkin National Medical Research Center, Novosibirsk, Russian Federation; Student of V. Zelman Institute of Medicine and Psychology, Novosibirsk State University, Novosibirsk, Russian Federation
Ilya A. Soynov
Meshalkin National Medical Research Center
Russian Federation
Russian Federation
PhD, MD, Head of the Department of Congenital Heart Disease Research, Meshalkin National Medical Research Center, Novosibirsk, Russian Federation
Yuriy Yu. Kulyabin
Meshalkin National Medical Research Center
Russian Federation
Russian Federation
PhD, Cardiovascular Surgeon, Department of Congenital Heart Disease Surgery, Research Fellow, Department of Congenital Heart Disease Research, Meshalkin National Medical Research Center, Novosibirsk, Russian Federation
Nataly R. Nichay
Meshalkin National Medical Research Center;
Novosibirsk State Medical University
Russian Federation
Russian Federation
PhD, Cardiovascular Surgeon, Department of Congenital Heart Disease Surgery, Research Fellow, Department of Congenital Heart Disease Research, Meshalkin National Medical Research Center, Novosibirsk, Russian Federation; Assistant Department of Cardiovascular Surgery, Novosibirsk State Medical University, Novosibirsk, Russian Federation
Kseniya A. Rzaeva
Almazov National Medical Research Center
Russian Federation
Russian Federation
PhD, Endovascular Surgeon, Almazov National Medical Research Center, Saint Petersburg, Russian Federation
Olga S. Anikina
Meshalkin National Medical Research Center
Russian Federation
Russian Federation
Anesthesiologist and Intensive Care Physician, Meshalkin National Medical Research Center, Novosibirsk, Russian Federation
Ilya A. Velyukhanov
Meshalkin National Medical Research Center
Russian Federation
Russian Federation
Head of the Pediatric Intensive Care Unit, Meshalkin National Medical Research Center, Novosibirsk, Russian Federation
Alex N. Arkhipov
Meshalkin National Medical Research Center
Russian Federation
Russian Federation
PhD, Head of the Department of Congenital Heart Disease, Meshalkin National Medical Research Center, Novosibirsk, Russian Federation
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51.
Review
For citations:
Amansakhatova E.N., Soynov I.A., Kulyabin Yu.Yu., Nichay N.R., Rzaeva K.A., Anikina O.S., Velyukhanov I.A., Arkhipov A.N. THE 1st STAGE OF HEMODYNAMIC STRATEGIES FOR MANAGEMENT OF HYPOPLASTIC LEFT HEART SYNDROME. Complex Issues of Cardiovascular Diseases. 2026;15(1):109-125. (In Russ.) https://doi.org/10.17802/2306-1278-2026-15-1-109-125
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